Thank you everyone, not sure what the future holds, what the prognosis is, there is no treatment so its a case of helping him the best we can to have a happy life.
Hubby will need to be tested to see if he carries the defect gene, if he does then the girls will need to be tested in the future.
It was an anxious wait for hubby to get home form work, we have cried alot, discussed alot, sat in silence, hugged and I feel utterly drained now but also relief that the wait is over and we now know the situation and we are no longer in limbo so to speak, well we are abit as we don't know whats going to happen. God I'm rambling now, off to bed but thank you again.